Qoraa: William Ramirez
Taariikhda Abuurista: 20 Setembar 2021
Taariikhda Cusboonaysiinta: 1 Julay 2024
Anonim
An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin
Dareemoleyad: An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin

Telangiectasias waa xididdada dhiigga ee maqaarka ku ballaaran. Badanaa dhib ma leh, laakiin waxaa laga yaabaa inay la xiriiraan dhowr cudur.

Telangiectasias ayaa laga yaabaa inuu ku kobco meel kasta oo jirka ka mid ah. Laakiin waxaa sida ugu fudud loogu arkaa maqaarka, xuubabka xuubka, iyo caddaanta indhaha. Badanaa, iyagu ma sababaan astaamo. Qaar ka mid ah telangiectasias ayaa dhiig baxa oo sababa dhibaatooyin waaweyn. Telangiectasias sidoo kale waxay ku dhici kartaa maskaxda ama xiidmaha waxayna sababi kartaa dhibaatooyin waaweyn dhiig baxa.

Sababaha waxaa ka mid noqon kara:

  • Rosacea (dhibaatada maqaarka ee keenta in wajigu casaan noqdo)
  • Gabow
  • Dhibaatada hiddo-wadaha
  • Uurka
  • Qorrax soo baxa
  • Xididdada xididdada
  • Isticmaalidda kareemada steroid
  • Uur ku taalo aagga

Cudurada la xiriira xaaladan waxaa ka mid ah:

  • Ataxia-telangiectasia (cudur ku dhaca maqaarka, isu dheelitirka iyo isku-duwidda, iyo meelaha kale ee jirka)
  • Bloom Syndrome (cudur la iska dhaxlo oo sababa dherer gaaban, xasaasiyadda maqaarka ee falaadhaha ultraviolet-ka ee qorraxda, iyo casaanka wejiga)
  • Cutis marmorata telangiectatica congenita (cudurka maqaarka oo keena dheecaan casaan)
  • Cilmiga telangiectasia ee dhiigbaxa (Osler-Weber-Rendu syndrome)
  • Klippel-Trenaunay-Weber syndrome (cudur sababa wasakhda dekedda-khamriga, xididdada dhiigga, iyo dhibaatooyinka unugyada jilicsan)
  • Nevus flammeus sida wasakhda dekedda-khamriga
  • Rosacea (xaalad maqaarka oo keenta wajiga casaan)
  • Cudurka Sturge-Weber (cudur ku lug leh wasakhda dekedda-khamriga iyo dhibaatooyinka nidaamka neerfaha)
  • Xeroderma pigmentosa (cudur maqaarka iyo sidoo kale unugyada daboolaya isha aad ugu nugul yihiin iftiinka ultraviolet)
  • Lupus (cudurka habka difaaca jirka)
  • Cudurka 'CREST Syndrome' (nooc ka mid ah cudurka 'scleroderma' oo ku lug leh soo saarista unugyo nabar u eg oo maqaarka ku dhaca iyo meelo kale oo jirka ka mid ah waxayna dhaawacdaa unugyada ku dhegsan derbiyada xididdada yaryar)

Wac daryeel caafimaad bixiyahaaga haddii aad ku aragto maraakiibta sii ballaaraneysa maqaarka, xuubabka xuubka, ama indhaha.


Bixiyaha ayaa sameyn doona baaritaan jireed wuxuuna weydiin doonaa astaamahaaga, oo ay ka mid yihiin:

  • Aaway xididdada dhiiggu?
  • Miyay si fudud oo aan sabab lahayn u dhiig baxaan?
  • Maxay yihiin calaamadaha kale ee jira?

Tijaabooyinka ayaa loo baahan karaa si loo ogaado ama looga saaro xaalad caafimaad. Tijaabooyinka waxaa ka mid noqon kara:

  • Tijaabooyinka dhiigga
  • Sawirada CT
  • Barashada shaqada beerka
  • Skaanka MRI
  • Raajo

Sclerotherapy waa daaweynta telangiectasias lugaha. Nidaamkan, xalka cusbada (milixda) ama kiimiko kale ayaa si toos ah loogu duraa xididdada caaro ee lugaha. Daaweynta laser-ka ayaa caadi ahaan loo isticmaalaa in lagu daaweeyo telangiectasias ee wajiga.

Ectasias xididdada dhiigga; Cudurka 'Spider angioma'

  • Angioma serpiginosum
  • Telangiectasia - lugaha
  • Telangiectasias - gacanta kore

Kelly R, Baker C. Cilladaha kale ee xididdada dhiigga. Gudaha: Bolognia JL, Schaffer JV, Cerroni L, eds. Cudurka maqaarka. 4aad. Philadelphia, PA: Elsevier; 2018: cutubka 106.


Patterson JW. Burooyinka xididdada dhiigga. Gudaha: Patterson JW, ed. Cudurka Maqaarka ee Weedon. 4aad. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: cutubka 38.

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