Acid mucopolysaccharides

Acid mucopolysaccharides waa baaritaan cabbiraya xaddiga mucopolysaccharides-ka lagu sii daayo kaadida hal dhacdo ama muddo ka badan 24-saac.

Mucopolysaccharides waa silsilado dhaadheer oo ku jira maaddooyinka sonkorta ee jirka ku jira. Badanaa waxaa laga helaa xabka iyo dareeraha agagaarka kala-goysyada.

Imtixaanka 24-ka saac ah, waa inaad ku kaadisaa bac ama weel gaar ah mar kasta oo aad musqusha isticmaasho. Badanaa, waxaa lagu siin doonaa laba weel. Waxaad si toos ah ugu kaadi doontaa weelka yar ee gaarka ah ka dibna kaadidaas waxaad ugu wareejin doontaa weelka kale ee weyn.

• Maalinta 1, ku kaadi musqusha markii aad subaxda ka soo kacdid.
• Kaadida ugu horeysa kadib, ku kaadi kaadi weelka gaarka ah markasta oo aad musqusha isticmaasho 24ka saacadood ee soo socda. Kaadida ku wareeji weelka weyn oo weelka weyn ku hay meel qabow ama tallaagad. Weelkan si adag u xir dabool.
• Maalinta 2aad, ku kaadi kaadi weelka subaxa labaad markale markaad toosto oo ku wareeji kaadidan weelka weyn.
• Ku calaamade weelka weyn magacaaga, taariikhda, waqtiga dhammaystirka, kuna soo celi sidii laguu faray.

Ilmaha yar:

Si fiican u maydho agagaarka kaadi mareenka (godka ay kaadidu ka baxdo). Fur boorsada kaadida lagu uruuriyo (bac balaastik ah oo warqad xabag leh ku leh dhinac dhinac).

• Ragga, guska oo dhan bacda ku dheji warqadda dhejiska leh maqaarka.
• Dheddigga, boorsada dusha ka saar labada laab ee maqaarka siilka labada dhinac (siilka). Ku xafaayad xafaayad ilmaha (bacda dusheeda).

Had iyo jeer hubi ilmaha, oo bacda ka beddel ka dib marka ilmuhu kaadiyo. Kaadida kaadida bacda ku shub weelka uu ku siinayo daryeel caafimaad bixiyahaaga.

Ilmaha firfircoon ayaa dhaqaajin kara bacda, taasoo keeneysa in kaadi ay gasho xafaayadda. Waxaa laga yaabaa inaad u baahato boorsooyin dheeraad ah.

Markaad dhamayso, calaamadee weelka oo ku soo celi sidii laguu sheegay.

Ma jiro diyaar garow gaar ah oo loo baahan yahay.

Tijaabadu waxay ku lug leedahay oo keliya kaadida caadiga ah, mana jiraan wax dhib ah.

Tijaabadan waxaa loo sameeyaa in lagu baaro koox dhif ah oo ku dhacda hiddo-wadaha loo yaqaan 'mucopolysaccharidoses' (MPS). Kuwaas waxaa ka mid ah, Hurler, Scheie, iyo xanuunnada Hurler / Scheie (MPS I), Hunter syndrome (MPS II), Sanfilippo syndrome (MPS III), Morquio syndrome (MPS IV), Maroteaux-Lamy syndrome (MPS VI), iyo Sly syndrome (MPS VII).

Waqtiga intiisa badan, baaritaankaan waxaa lagu sameeyaa dhallaanka laga yaabo inay yeeshaan astaamo ama taariikh qoys oo ka mid ah cilladahaan.

Heerarka caadiga ah waxay ku kala duwan yihiin da'da iyo shaybaarka ilaa sheybaarka. Kala hadal adeeg bixiyahaaga macnaha natiijooyinka baaritaankaaga gaarka ah.

Heerarka aan caadiga ahayn ee sarreeya waxay la jaan qaadi karaan nooc ka mid ah xuubka dheecaanka loo yaqaan 'mucopolysaccharidosis'. Tijaabooyin dheeri ah ayaa loo baahan yahay si loo ogaado nooca gaarka ah ee loo yaqaan 'mucopolysaccharidosis'.

AMP; Dermatan sulfate - kaadida; Kaadi-hepataran kaadida; Kaadi-dhiigga dermatan sulfate; Heparan sulfate - kaadi

Kumar V, Abbas AK, Aster JC. Cilladaha hidaha. In: Kumar V, Abbas AK, Aster JC, eds. Robbins iyo Cotran Pathologic Aasaaska Cudurka. 9aad. Philadelphia, PA: Elsevier Saunders; 2015: cutubka 5.

Xaraashka JW. Mucopolysaccharidoses. Gudaha: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Buugga Buugga Caafimaadka Caruurta. 21aad ed. Philadelphia, PA: Elsevier; 2020: cutubka 107.

Turnpenny PD, Ellard S. Khaladaadka ku dhasha dheef-shiid kiimikaadka. Gudaha: Turnpenny PD, Ellard S, eds. Waxyaabaha Emergy ee Cilmiga Caafimaadka. 15aad. Philadelphia, PA: Elsevier; 2017: cutubka 18.