Qoraa: Virginia Floyd
Taariikhda Abuurista: 12 Ogost 2021
Taariikhda Cusboonaysiinta: 20 Juun 2024
Anonim
Congenital adrenal hyperplasia : Etiology ,Pathophysiology ,Clinical features ,Diagnosis ,Treatment
Dareemoleyad: Congenital adrenal hyperplasia : Etiology ,Pathophysiology ,Clinical features ,Diagnosis ,Treatment

17-OH progesterone waa baaritaan dhiig oo cabiraya qadarka 17-OH progesterone. Kani waa hormoon ay soo saaraan qanjidhada adrenal iyo qanjidhada galmada.

Sambal dhiig ayaa loo baahan yahay. Inta badan, dhiig ayaa laga soo qaataa xididka ku yaal gudaha xusulka ama dhabarka gacanta.

Dhallaanka ama carruurta yaryar, qalab fiiqan oo loo yaqaan 'lancet' ayaa loo isticmaali karaa in lagu mudo maqaarka.

  • Dhiiggu wuxuu ku ururiyaa tuubbo yar oo dhalo ah oo loo yaqaanno 'pipe', ama ku soo duub ama aaladda wax lagu baaro.
  • Faashad ayaa la dul dhigayaa meesha si loo joojiyo wax dhiig bax ah.

Daawooyin badan ayaa faragelin kara natiijooyinka baaritaanka dhiigga.

  • Bixiyahaaga daryeelka caafimaad ayaa kuu sheegi doona haddii aad u baahan tahay inaad joojiso qaadashada wax daawo ah ka hor baaritaankaan.
  • Ha joojin ama ha beddelin daawooyinkaaga adiga oo aan marka hore la hadlin takhtarkaaga.

Waxaa laga yaabaa inaad dareento xanuun yar ama qaniinyo markii cirbadda la gelinayo. Waxa kale oo laga yaabaa inaad dareento xoogaa jug ah goobta ka dib markii dhiigga lagaa qaado.

Isticmaalka ugu weyn ee baaritaankaan waa in laga hubiyo dhallaanka cillad la iska dhaxlo oo saameysa qanjirka 'adrenal gland', oo loo yaqaan 'congenital adrenal hyperplasia' (CAH). Waxaa badanaa lagu sameeyaa dhallaanka ku dhasha xubnaha taranka ee dibadda oo aan si muuqata ugu muuqan kuwa wiilka ama gabadha.


Tijaabadan waxaa sidoo kale loo isticmaalaa in lagu aqoonsado dadka ku dhaca astaamaha CAH noloshooda dambe, xaalad loo yaqaan nonclassical adrenal hyperplasia.

Bixiye ayaa kula talin kara baaritaankaan dumarka ama gabdhaha leh astaamo lab sida:

  • Kordhinta timaha xad dhaafka ah ee meelaha ragga waaweyn ay timo ku koraan
  • Cod qoto dheer ama kordhinta murqaha
  • Maqnaanshaha caadada
  • Madhalaysnimo

Qiyamyada caadiga ah iyo kuwa aan caadiga ahayn waxay ku kala duwan yihiin carruurta dhasha miisaankoodu hooseeyo. Guud ahaan, natiijooyinka caadiga ah waa sida soo socota:

  • Ilmuhu in ka badan 24 saacadood - in ka yar 400 illaa 600 nanogram halkii deciliter (ng / dL) ama 12.12 ilaa 18.18 nanomoles halkii litir (nmol / L)
  • Carruurta ka hor qaangaadhnimada qiyaastii 100 ng / dL ama 3.03 nmol / L
  • Dadka waaweyn - in ka yar 200 ng / dL ama 6.06 nmol / L

Heerarka qiimaha caadiga ahi way ku kala duwanaan karaan shaybaarada kala duwan. Kala hadal adeeg bixiyahaaga macnaha natiijooyinka baaritaankaaga gaarka ah.

Tusaalooyinka kore waxay muujinayaan cabirka guud ee natiijooyinka imtixaanadan. Shaybaarada qaarkood waxay isticmaalaan cabbiro kala duwan ama waxay tijaabin karaan tijaabooyin kala duwan.


Heer sare oo ah progesterone 17-OH ayaa sababi kara:

  • Burooyinka qanjidhada adrenal
  • Dhalmada adrenal hyperplasia (CAH)

Dhallaanka qaba CAH, heerka 17-OHP wuxuu u dhexeeyaa 2,000 ilaa 40,000 ng / dL ama 60.6 ilaa 1212 nmol / L. Dadka qaangaarka ah, heer ka weyn 200 ng / dL ama 6.06 nmol / L ayaa laga yaabaa inay sabab u tahay non-classical adrenal hyperplasia.

Bixiyahaagu wuxuu kuu soo jeedin karaa baaritaanka ACTH haddii heerka progesterone 17-OH uu u dhexeeyo 200 ilaa 800 ng / dL ama 6.06 ilaa 24.24 nmol / L.

17-hydroxyprogesterone; Progesterone - 17-OH

Guber HA, Farag AF. Qiimeynta shaqada endocrine. Gudaha: McPherson RA, Pincus MR, eds. Henry's Clinical Diagnosis iyo Maareynta Hababka Shaybaarka. 23aad ed. St Louis, MO: Elsevier; 2017: cutubka 24.

Rey RA, Josso N. Ciladda iyo daaweynta ciladaha horumarka galmada. Gudaha: Jameson JL, De Groot LJ, de Kretser DM, et al, eds. Endocrinology: Dadka waaweyn iyo carruurta. 7aad ed. Philadelphia, PA: Elsevier Saunders; 2016: cutubka 119.

PC-ga cad. Cudurka 'hypertlasia adrenal hyperplasia' iyo cilladaha la xiriira. Gudaha: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Buugga Buugga Caafimaadka Caruurta. 21aad ed. Philadelphia, PA: Elsevier; 2020: baab 594.


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