Tijaabooyinka Porphyrin

Qanacsan

• Waa maxay tijaabooyinka porphyrin?
• Maxaa loo adeegsadaa?
• Maxaan ugu baahanahay baaritaanka porphyrin?
• Maxaa dhacaya inta lagu jiro baaritaanka porphyrin?
• Ma u baahanahay inaan sameeyo wax walba si aan ugu diyaargaroobo imtixaanka?
• Ma jiraan wax khatar ah oo ku iman kara tijaabooyinka porphyrin?
• Maxay natiijooyinka ka dhigan yihiin?
• Ma jiraan wax kale oo aan u baahanahay inaan ka ogaado baaritaanka borogaraamyada?
• Tixraacyo

Waa maxay tijaabooyinka porphyrin?

Baadhitaanada 'Porphyrin' ayaa lagu cabiraa heerka bogsiga dhiiggaaga, kaadidaada, ama saxaradaada. Porphyrins waa kiimiko ka caawisa sameynta haemoglobin, nooc ka mid ah borotiinka ku jira unugyada dhiigga cas. Hemoglobin wuxuu oksijiinka ka qaadaa sambabadaada ilaa jirka intiisa kale.

Waa wax caadi ah in waxoogaa yar oo faleebooyin ah laga helo dhiiggaaga iyo dheecaannada kale ee jirka. Laakiin porphyrin aad u badan ayaa macnaheedu noqon karaa inaad leedahay nooc ka mid ah bolofiska. Cudurka loo yaqaan 'Porphyria' waa cillad naadir ah oo sababi karta dhibaatooyin caafimaad oo daran. Porphyria badanaa waxaa loo qaybiyaa laba qaybood:

• Cudurka faafa ee daran, taas oo inta badan saameyn ku yeelata habdhiska neerfaha isla markaana sababa calaamadaha caloosha
• Boorashka maqaarka, oo sababa astaamaha maqaarka marka aad u iftiimiso iftiinka qoraxda

Qaar ka mid ah porphyrias waxay saameeyaan nidaamka neerfaha iyo maqaarka labadaba.

Magacyada kale: protoporphyrin; protoporphyrin, dhiig; protoporhyrin, saxarada; porphyrins, saxarada; uroporphyrin; porphyrins, kaadida; Imtixaanka Mauzerall-Granick; aashito; ALA; porphobilinogen; PBG; etopiocyte protoporphyrin lacag la’aan ah; jajabinta erythrocyte porphyrins; FEP

Maxaa loo adeegsadaa?

Baadhitaanada loo yaqaan 'Porphyrin' ayaa loo isticmaalaa in lagu baaro ama loola socdo xanuunka loo yaqaan 'porphyria'.

Maxaan ugu baahanahay baaritaanka porphyrin?

Waxaa laga yaabaa inaad u baahato baaritaanka porphyrin haddii aad isku aragto astaamo u eg in lagaa qaado. Waxaa jira calaamado kala duwan oo noocyada kala duwan ee loo yaqaan 'porphyria'.

Astaamaha cudurka daran ee loo yaqaan 'porphyria' waxaa ka mid ah:

• Calool xanuun
• Calool fadhiga
• Lalabbo iyo matag
• Kaadi cas ama bunni ah
• Cirrid ama xanuun gacmaha iyo / ama cagaha
• Murqaha oo daciifa
• Jahwareer
• Hallucinations

Astaamaha xanuunka loo yaqaan 'porphyria' waxaa kamid ah:

• Xasaasiyad xagga qorraxda ah
• Nabaro maqaarka ku yaal oo u soo baxaya iftiinka qoraxda
• Guduudasho iyo barar maqaarka soo gaadhay
• Cuncun
• Isbedelada midabka maqaarka

Waxa kale oo laga yaabaa inaad u baahato baaritaanka porphyrin haddii qof qoyskaaga ka mid ahi qabo cudurka loo yaqaan 'porphyria'. Noocyada ugu badan ee loo yaqaan 'porphyria' waa kuwo la iska dhaxlo, taasoo la micno ah in cudurka uu ka gudbo waalidka una gudbo ilmaha.

Maxaa dhacaya inta lagu jiro baaritaanka porphyrin?

Porphyrins waxaa lagu baari karaa dhiig, kaadida, ama saxarada. Noocyada ugu caansan ee baaritaanka porphyrin ayaa hoos ku taxan.

• Tijaabada Dhiigga
  • Xirfadlaha daryeelka caafimaadka ayaa tijaabo dhiig ka qaadi doona xididka gacantaada, isagoo isticmaalaya cirbad yar. Kaddib cirbada la geliyo, qadar yar oo dhiig ah ayaa lagu ururin doonaa tuubada baaritaanka ama fijaan. Waxaa laga yaabaa inaad dareento xoog wax yar ah markii irbadda ay soo galayso ama ay ka baxeyso. Tani badanaa waxay qaadataa in ka yar shan daqiiqo.
• 24-Saac Muunad Kaadi ah
  • Waxaad ururin doontaa dhammaan kaadidaada muddo 24-saac ah. Tijaabadan, daryeel caafimaad bixiyahaaga ama shaybaarka ayaa ku siin doona konteenar iyo tilmaamo gaar ah oo ku saabsan sida shaybaaradaada loogu ururiyo guriga. Hubso inaad si taxaddar leh u raacdo tilmaamaha oo dhan. Tijaabadan tijaabada ah ee 24-ka saac ah ayaa loo isticmaalaa maxaa yeelay qaddarka maaddooyinka ku jira kaadida, oo ay ku jiraan porphyrin, way kala duwanaan karaan maalinta oo dhan. Marka uruurinta dhowr shaybaar maalintii waxay bixin kartaa sawir sax ah oo ku saabsan kaadidaada.
• Tijaabada Kaadida ee Random
  • Waad soo bandhigi kartaa shaybaarkaaga wakhti kasta oo maalintii ah, iyada oo aan loo baahnayn diyaargarow gaar ah ama wax ka qabasho. Tijaabadani waxaa badanaa lagu sameeyaa xafiiska bixiyaha daryeelka caafimaadka ama sheybaarka.
• Baaritaanka Saxarada (oo sidoo kale loogu yeero protoporphyrin saxarada)
  • Waxaad ururin doontaa saamiga saxaradaada oo waxaad ku ridi doontaa weel gaar ah. Bixiyaha daryeelka caafimaadkaaga ayaa ku siin doona tilmaamo ku saabsan sida loo diyaariyo shaybaarkaaga oo loogu diro shaybaarka.

Ma u baahanahay inaan sameeyo wax walba si aan ugu diyaargaroobo imtixaanka?

Uma baahnid wax diyaargarow gaar ah oo loogu talagalay baaritaanka dhiigga ama kaadida.

Baaritaanka saxarada, waxaa lagu farayaa inaadan cunin hilibka ama aadan qaadan wax daawo ah oo ay ku jirto asbiriin seddex maalmood baaritaankaaga ka hor.

Ma jiraan wax khatar ah oo ku iman kara tijaabooyinka porphyrin?

Khatar aad u yar baa jirta in dhiig lagaa qaado. Waxaa laga yaabaa inaad xanuun yar ama nabar ku yeelato barta irbadda lagu muday, laakiin astaamaha badankood si dhakhso leh ayey u baxaan.

Ma jiraan wax khatar ah oo la og yahay oo ku imanaya baadhitaanka kaadida ama saxarada.

Maxay natiijooyinka ka dhigan yihiin?

Haddii heerarka sare ee porphyrin laga helo dhiiggaaga, kaadidaada, ama saxaradaada, bixiyaha xanaanada caafimaadkaaga ayaa laga yaabaa inuu dalbado baaritaano dheeri ah si loo xaqiijiyo ogaanshaha cudurka iyo in la ogaado nooca booriyada aad leedahay. In kasta oo aan daawo loo helin xanuunka loo yaqaan 'porphyria', haddana xaaladda waa la maareyn karaa. Isbedelada nolosha qaarkood iyo / ama daawooyinka ayaa kaa caawin kara kahortaga astaamaha iyo dhibaatooyinka cudurka. Daaweynta qaaska ah waxay kuxirantahay nooca porphyria ee aad leedahay. Haddii aad qabtid su'aalo ku saabsan natiijooyinkaaga ama ku saabsan cudurka loo yaqaan 'porphyria', kala hadal daryeel caafimaad bixiyahaaga.

Wax badan ka baro baaritaanka shaybaarka, kala duwanaanshaha tixraaca, iyo fahamka natiijooyinka.

Ma jiraan wax kale oo aan u baahanahay inaan ka ogaado baaritaanka borogaraamyada?

In kasta oo noocyada ugu badan ee loo yaqaan 'porphyria' la iska dhaxlo, noocyo kale oo kale ayaa sidoo kale la heli karaa. Cudurka 'porphyria' ee la soo qaaday waxaa sababi kara arrimo kala duwan, oo ay ka mid yihiin soo-gaadhis saa'id ah oo leedh ah, HIV, cagaarshowga C, qaadashada macdanta birta ee xad-dhaafka ah, iyo / ama isticmaalka khamriga culus.

Tixraacyo

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Macluumaadka ku yaal boggan waa in aan loo isticmaalin beddel daryeel caafimaad oo xirfad leh ama talo. La xiriir bixiye daryeel caafimaad haddii aad su'aalo ka qabtid caafimaadkaaga.