Qoraa: Clyde Lopez
Taariikhda Abuurista: 21 Julay 2021
Taariikhda Cusboonaysiinta: 1 Julay 2024
Anonim
Retroperitoneal Fibrosis
Dareemoleyad: Retroperitoneal Fibrosis

Cudurka 'Retroperitoneal fibrosis' waa cillad naadir ah oo xirta tuubooyinka (kaadi mareennada) kaadida ka qaada kilyaha illaa kaadi haysta.

Cudurka 'Retroperitoneal fibrosis' wuxuu dhacaa marka unugyo dheeri ah oo buurnaan ahi ay ku sameysmaan aagga ka dambeeya caloosha iyo mindhicirada. Cadka ayaa sameeya cuf (ama cuf) ama unug adag oo fibrotic ah. Waxay xannibi kartaa tuubooyinka kaadida ka qaada kilyaha ilaa kaadiheysta.

Sababta dhibaatadan badanaa lama yaqaan. Wuxuu ku badan yahay dadka jira 40 ilaa 60. Ragga waxay laba jeer uga dhow yihiin inay ku soo boodaan xaaladda dumarka.

Calaamadaha hore:

  • Xanuun calool xanuun ah oo caloosha ku sii siyaada waqti ka dib
  • Xanuun iyo midab beddel lugaha ah (socodka dhiigga oo yaraaday awgeed)
  • Barar hal lug ah

Astaamaha dambe:

  • Kaadida oo yaraatay
  • Soo bixid kaadi la'aan (anuria)
  • Lalabbo, matag, isbeddellada xaaladda maskaxeed ee ay sababaan kalyaha oo shaqeynaya iyo kiimikooyin sun ah oo dhiigga ku soo kordha
  • Xanuun daran oo caloosha ah oo leh dhiig ku jira saxarada (sababtoo ah dhimashada unugyada xiidmaha)

Sawirka CT-ga caloosha ayaa ah habka ugu wanaagsan ee lagu helo tiro dib-u-habeyn ah.


Tijaabooyinka kale ee ka caawin kara baaritaanka xaaladan waxaa ka mid ah:

  • BUN iyo baaritaanka dhiigga creatinine
  • Pyelogram-ka xididka la siiya (IVP), oo aan sida caadiga ah loo isticmaalin
  • Qalabka kelyaha
  • MRI caloosha
  • Baadhitaanka 'CAT' ee caloosha iyo 'retroperitoneum'

Cad ka-qaadista cufnaanta jirka ayaa sidoo kale la samayn karaa si meesha looga saaro kansarka.

Corticosteroids ayaa marka hore la tijaabiyaa. Qaar ka mid ah bixiyeyaasha xanaanada caafimaadka ayaa waliba qoro daawo loo yaqaan tamoxifen.

Haddii daaweynta corticosteroid aysan shaqeynin, biopsy waa in la sameeyaa si loo xaqiijiyo cudurka. Daawooyinka kale ee lagu xakameynayo nidaamka difaaca jirka waa la qori karaa.

Marka daawadu shaqeyn weydo, qalliin iyo doog (tubbada dheecaanka) ayaa loo baahan yahay.

Aragtida waxay ku xirnaan doontaa baaxadda dhibaatada iyo xaddiga waxyeelada kelyaha.

Dhaawaca kiliyaha wuxuu noqon karaa mid ku meel gaar ah ama joogto ah.

Ciladda waxay u horseedi kartaa:

  • Xannibaadda socda ee tuubooyinka ka soo baxa kelyaha mid ama labada dhinacba
  • Kelyo la'aan joogto ah

Wac adeeg bixiyahaaga haddii aad leedahay calool xanuun hoose ama garab dhinac ah iyo wax soo saar yar oo kaadi ah.


Isku day inaad iska ilaaliso isticmaalka muddada-dheer ee daawooyinka ay ku jiraan methysergide. Daawadan ayaa la muujiyay inay sababi karto cudurka 'fibro' ee loo yaqaan 'retroperitoneal fibrosis'. Methysergide waxaa mararka qaar loo isticmaalaa in lagu daaweeyo madax xanuunka dhanjafka.

Idiopathic retroperitoneal fibrosis; Cudurka Ormond

  • Nidaamka kaadi-mareenka ragga

Comperat E, Bonsib SM, Cheng L. Miskaha miskaha iyo kaadi mareenka. Gudaha: Cheng L, MacLennan GT, Bostwick DG, eds. Cudurka Qalliinka Urologic. 4aad. Philadelphia, PA: Elsevier; 2020: cutubka 3.

Nakada SY, Best SL. Maareynta xannibaadda marinka kaadi mareenka sare. Gudaha: Wein AJ, Kavoussi LR, Partin AW, Peters, CA, eds. Campbell-Walsh Urolojiga. 11aad. Philadelphia, PA: Elsevier; 2016: cutubka 49.

O'Connor OJ, Maher MM. Mareenka kaadi mareenka: dulmar guud oo ku saabsan qaab dhismeedka jirka, farsamooyinka iyo arrimaha shucaaca. Gudaha: Adam A, Dixon AK, Gillard JH, Schaefer-Prokop CM, eds. Raajada Raadinta ee Grainger & Allison: Buugga Buugga Sawirka Caafimaadka. 6aad ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2015: cutubka 35.


Shanmugam VK. Vasculitis iyo arteriopathies kale oo aan caadi ahayn. Gudaha: Sidawy AN, Perler BA, eds. Qalliinka Rutherford ee Vascular and Endovascular Therapy. 9aad. Philadelphia, PA: Elsevier; 2019: cutubka 137.

Turnage RH, Mizell J, Badgwell B. Darbiga Caloosha, xudunta, peritoneum, mesenteries, omentum, iyo retroperitoneum. Gudaha: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Sabiston Buugga Qalitaanka. 20aad. Philadelphia, PA: Elsevier Saunders; 2017: cutubka 43.

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