Cudurka caloosha ee 'Prune'

Cudurka caloosha ee loo yaqaan 'Prune belly syndrome' waa koox cilladaha dhalashada ee dhifka ah ee ku lug leh seddexdan dhibaato ee ugu waaweyn:
- Kobcin liidata oo muruqyada caloosha ah, taasoo keenta in maqaarka aagga caloosha uu u ruxo sida manjooyin
- Xiniinyaha Undescised
- Dhibaatooyinka kaadi mareenka
Sababaha saxda ah ee cudurka manjooyinka caloosha manjo lama yaqaan. Xaaladda ayaa ku dhacda inta badan wiilasha.
Inta uu caloosha kujiro, caloosha cunuga soo koraya ayaa dheecaan ku biirayaa. Badanaa, sababta ayaa dhibaato ku ah marinka kaadi mareenka. Dareeraha ayaa baaba'a dhalashada kadib, taasoo keenta calool duuban oo u eg manjooyin. Muuqaalkani waa mid la ogaan karo sababtoo ah la'aanta muruqyada caloosha.
Muruqyada caloosha oo daciifa ayaa sababi kara:
- Calool fadhiga
- Dib u dhig fadhiga iyo socodka
- Dhibaatooyinka qufaca
Dhibaatooyinka kaadi mareenka waxay u horseedi karaan kaadi la'aan.
Haweeney uur leh ilmo qabta cillad caloosha ah ayaa laga yaabaa inaanay yeelan dheecaan amniotic ah (dheecaanka ku xeeran uurjiifka). Tani waxay sababi kartaa ilmaha yar inuu yeesho dhibaatooyin sanbabada ah oo la cadaadiyo caloosha.
Ultrasound-ka la sameeyo muddada uurka wuxuu muujin karaa in ilmuhu leeyahay kaadiheysta oo barara ama kelyaha weynaaday.
Xaaladaha qaarkood, ultrasound-ka uurka ayaa sidoo kale kaa caawin kara go'aaminta haddii ilmuhu leeyahay:
- Dhibaatooyinka wadnaha
- Lafo ama murqo aan caadi ahayn
- Caloosha iyo dhibaatooyinka xiidmaha
- Sambabaha oo aan horumarin
Tijaabooyinka soo socda ayaa lagu samayn karaa ilmaha dhalashada ka dib dhalashada si loo ogaado xaaladda:
- Tijaabooyinka dhiigga
- Pyelogram-ka xididka xididka (IVP)
- Ultrasound
- Faaruqa cystourethrogram (VCUG)
- Raajo
- CT iskaanka
Qalliinka hore waxaa lagula talinayaa in lagu xaliyo muruqyada caloosha oo daciifka ah, dhibaatooyinka marinka kaadi mareenka, iyo xiniinyaha aan la rabin.
Ilmaha waxaa la siin karaa antibiyootiko si loogu daaweeyo ama looga hortago infekshinka kaadi mareenka.
Kheyraadka soo socda ayaa bixin kara macluumaad dheeri ah oo ku saabsan manjarka caloosha:
- Shabakadda Prune Belly Syndrome - prunebelly.org
- Ururka Qaranka ee Dhibaatooyinka Nadir - rarediseases.org/rare-diseases/prune-belly-syndrome
Cudurka caloosha ee loo yaqaan 'Prune belly syndrome' waa dhibaato halis ah oo badiyaa nafta halis gelisa.
Dhallaanka badan ee xaaladan leh waa kuwo weli dhasha ama dhinta toddobaadyada ugu horreeya noloshooda. Sababta dhimashadu waxay ka timaaddaa sambabada ama dhibaatooyinka kelyaha oo daran, ama dhibaatooyinka isku dhafka ee dhalashada.
Dhallaanka cusubi way badbaadaan oo si caadi ah ayey u kori karaan. Qaar kale waxay leeyihiin dhibaatooyin caafimaad oo badan iyo koritaan.
Dhibaatooyinka waxay kuxiranyihiin dhibaatooyinka laxiriira. Kuwa ugu caansan waa:
- Calool fadhiga
- Cilladaha lafaha (cagaha lugta, sinta kala go'day, addinka oo maqan, farta, ama suulka, xabadka fanka)
- Cudurka marinka kaadi mareenka (wuxuu u baahan karaa sifayn iyo kalyo-beddelid)
Xiniinyaha oo aan laga fiirsan ayaa u horseedi kara madhalaysnimo ama kansar.
Cudurka 'Prune belly syndrome' waxaa badanaa la ogaadaa dhalashada ka hor ama markuu ilmuhu dhasho.
Haddii aad haysato cunug laga helay cudurka manjarka caloosha, ka wac daryeel caafimaad bixiyahaaga calaamadda ugu horreysa ee caabuqa kaadi mareenka ama calaamadaha kale ee kaadi mareenka.
Haddii ultrasound-ka uurka uu muujiyo in ilmahaagu leeyahay kaadiheysta oo barara ama kelyaha weynaaday, la hadal takhasusle uurka ku jira halista sare ama perinatology.
Ma jirto hab la yaqaan oo looga hortago xaaladdan. Haddii ilmuhu laga helo xannibaadda kaadi mareenka kahor dhalashadiisa, xaalado dhif ah, qalliin inta lagu guda jiro uurka waxay ka caawin kartaa ka hortagga dhibaatada inay u sii gudubto cudurka caloosha.
Cilladda Eagle-Barrett; Cudurka 'Triad syndrome'
Caldamone AA, Diiday FT. Cudurka 'Prune-belly syndrome'. Gudaha: Wein AJ, Kavoussi LR, Partin AW, Peters CA, eds. Campbell-Walsh Urolojiga. 11aad. Philadelphia, PA: Elsevier; 2016: cutubka 140.
Oday JS. Cudurka kaadi mareenka. Gudaha: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Buugga Buugga Caafimaadka Caruurta. 21aad ed. Philadelphia, PA: Elsevier; 2020: baab 555.
Merguerian PA, Rowe CK. Cilladaha aan caadiga ahayn ee koritaanka nidaamka genitourinary. Gudaha: Gleason CA, Juul SE, eds. Cudurada Avery ee Dhasha. 10aad ed. Philadelphia, PA: Elsevier; 2018: cutubka 88.