Wiskott-Aldrich syndrome

Qanacsan

• Calaamadaha cudurka Wiskott-Aldrich Syndrome
• Daaweynta Wiskott-Aldrich Syndrome

Cilmiga Wiskott-Aldrich waa cudur ku dhaca hidde-sideyaasha, kaas oo waxyeelleeya nidaamka difaaca jirka ee ku lug leh T iyo B lymphocytes, iyo unugyada dhiigga ee ka caawiya xakameynta dhiigbaxa, xinjirowga.

Calaamadaha cudurka Wiskott-Aldrich Syndrome

Calaamadaha Wiskott-Aldrich syndrome waxay noqon karaan:

U janjeedha dhiig-baxa:

• Hoos udhaca tirada iyo cabirka platelets-ka dhiiga kujira;
• Dhiigbax goos goos ah oo lagu garto dhibco casaan-buluug ah oo cabbirkiisu le'eg yahay madaxa madaxa, oo loo yaqaan "petechiae", ama way sii weynaan karaan oo waxay u egyihiin nabarro;
• Saxaro dhiig leh (gaar ahaan carruurnimada), ciridka oo dhiig baxa iyo sanka oo dheecaan ka baxa.

Infekshannada soo noqnoqda ee ay sababaan dhammaan noocyada noolaha sida:

• Otitis media, sinusitis, oof wareen;
• Qoorgooyaha, oof-wareenka oo ay keento Pneumocystis jirveci;
• Infekshinka maqaarka ee fayraska oo ay keento molluscum contagiosum.

Canbaarta:

• Infekshannada joogtada ah ee maqaarka;
• Dhibco madow oo maqaarka ah.

Muujinta otomatiga:

• Vasculitis;
• Dhiig yaraanta Hemolytic;
• Idiopathic thrombocytopenic purpura (Daaweynta dhiig-yaraanta wadnaha)

Baadhitaanka cudurkan waxaa samayn kara dhakhtarka carruurta ka dib marka uu kormeero caafimaad ee astaamaha iyo tijaabooyin gaar ah. Qiimeynta baaxadda platelet-ka waa mid ka mid ah hababka lagu ogaado cudurka, maadaama cuduro yar ay leeyihiin dabeecaddan.

Daaweynta Wiskott-Aldrich Syndrome

Daaweynta ugu habboon ee loo yaqaan 'Wiskott-Aldrich syndrome' waa tallaalidda dhuuxa lafta. Noocyada kale ee daaweynta waa ka saarida beeryarada, maadaama xubintani ay baabi'ineyso xaddiga yar ee ka mid ah platelet-ka ee dadka qaba cilladan ay qabaan, isticmaalka haemoglobin iyo isticmaalka antibayootigyada.

Cimriga dadka qaba cilladan cillad-darrada ah waa hooseysaa, kuwa badbaada markay toban jirka gaaraan caadi ahaan waxay yeeshaan burooyin sida lymphoma iyo leukemia.