Wiskott-Aldrich syndrome
Qanacsan
Cilmiga Wiskott-Aldrich waa cudur ku dhaca hidde-sideyaasha, kaas oo waxyeelleeya nidaamka difaaca jirka ee ku lug leh T iyo B lymphocytes, iyo unugyada dhiigga ee ka caawiya xakameynta dhiigbaxa, xinjirowga.
Calaamadaha cudurka Wiskott-Aldrich Syndrome
Calaamadaha Wiskott-Aldrich syndrome waxay noqon karaan:
U janjeedha dhiig-baxa:
- Hoos udhaca tirada iyo cabirka platelets-ka dhiiga kujira;
- Dhiigbax goos goos ah oo lagu garto dhibco casaan-buluug ah oo cabbirkiisu le'eg yahay madaxa madaxa, oo loo yaqaan "petechiae", ama way sii weynaan karaan oo waxay u egyihiin nabarro;
- Saxaro dhiig leh (gaar ahaan carruurnimada), ciridka oo dhiig baxa iyo sanka oo dheecaan ka baxa.
Infekshannada soo noqnoqda ee ay sababaan dhammaan noocyada noolaha sida:
- Otitis media, sinusitis, oof wareen;
- Qoorgooyaha, oof-wareenka oo ay keento Pneumocystis jirveci;
- Infekshinka maqaarka ee fayraska oo ay keento molluscum contagiosum.
Canbaarta:
- Infekshannada joogtada ah ee maqaarka;
- Dhibco madow oo maqaarka ah.
Muujinta otomatiga:
- Vasculitis;
- Dhiig yaraanta Hemolytic;
- Idiopathic thrombocytopenic purpura (Daaweynta dhiig-yaraanta wadnaha)
Baadhitaanka cudurkan waxaa samayn kara dhakhtarka carruurta ka dib marka uu kormeero caafimaad ee astaamaha iyo tijaabooyin gaar ah. Qiimeynta baaxadda platelet-ka waa mid ka mid ah hababka lagu ogaado cudurka, maadaama cuduro yar ay leeyihiin dabeecaddan.
Daaweynta Wiskott-Aldrich Syndrome
Daaweynta ugu habboon ee loo yaqaan 'Wiskott-Aldrich syndrome' waa tallaalidda dhuuxa lafta. Noocyada kale ee daaweynta waa ka saarida beeryarada, maadaama xubintani ay baabi'ineyso xaddiga yar ee ka mid ah platelet-ka ee dadka qaba cilladan ay qabaan, isticmaalka haemoglobin iyo isticmaalka antibayootigyada.
Cimriga dadka qaba cilladan cillad-darrada ah waa hooseysaa, kuwa badbaada markay toban jirka gaaraan caadi ahaan waxay yeeshaan burooyin sida lymphoma iyo leukemia.
Waxaan Kugula Talineynaa
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