IgA vasculitis - Henoch-Schönlein oo loo yaqaan 'vasculitis'

IgA vasculitis waa cudur ku lug leh baro buluug ah oo maqaarka ah, kalagoys xanuun, dhibaatooyinka caloosha, iyo glomerulonephritis (nooc cillad kelyo ah). Waxaa sidoo kale loo yaqaan Henoch-Schönlein purpura (HSP).

IgA vasculitis waxaa sababa jawaab celin aan caadi aheyn ee habka difaaca jirka. Natiijadu waa caabuq ku dhaca marinnada dhiigga ee cirka ku jira ee maqaarka. Xididdada dhiigga ee kala-goysyada, kilyaha, ama xiidmaha ayaa sidoo kale saameyn kara. Ma cadda sababta ay tani u dhacdo.

Cilladda cillad-xanuunka waxaa badanaa lagu arkaa carruurta da'doodu u dhexeyso 3 illaa 15 sano, laakiin waxaa laga yaabaa in lagu arko dadka waaweyn. Wuxuu ku badan yahay wiilasha marka loo eego gabdhaha. Dad badan oo cudurkaan ku dhaca wuxuu ku dhacay infekshinka sare ee neef mareenka toddobaadyadii ka horreeyay.

Calaamadaha iyo astaamaha IgA vasculitis waxaa ka mid noqon kara:

• Dhibco guduudan oo maqaarka ah (purpura). Tani waxay ku dhacdaa ku dhowaad dhammaan carruurta leh xaaladda. Tani badanaa waxay ku dhacdaa badhida, lugaha hoose, iyo xusullada.
• Calool xanuun.
• Xanuun wadajir ah.
• Kaadi aan caadi ahayn (waxaa laga yaabaa inuusan laheyn wax calaamado ah).
• Shuban, mararka qaar dhiig.
• Jeermiska ama anjioedema.
• Lalabbo iyo matag.
• Barar iyo xanuun ku dhaca xinjirta wiilasha.
• Madax xanuun.

Bixiyaha daryeelka caafimaadka ayaa eegi doona jirkaaga oo fiirin doona maqaarkaaga. Baadhitaanka jirka ayaa lagu arki doonaa nabarrada maqaarka (purpura, lesions) iyo danqasho wadajir ah.

Tijaabooyinka waxaa ka mid noqon kara:

• Kaadida waa in lagu sameeyaa kiisaska oo dhan.
• Tirinta dhiigga oo dhammaystiran. Platelet-ka wuxuu noqon karaa mid caadi ah.
• Baaritaanka xinjirowga: kuwani waa inay caadi ahaadaan.
• Cad ka-qaadista maqaarka, gaar ahaan dadka waaweyn.
• Baadhitaanada dhiiga si loo raadiyo sababaha kale ee keena caabuqa xididdada dhiigga, sida nidaamka lupus erythematosus, Vasculitis-ka la xidhiidha ANCA ama cagaarshowga.
• Dadka qaangaarka ah, waa in la sameeyaa baaritaanka kelyaha.
• Tijaabinta caloosha haddii xanuun jiro.

Ma jiro daaweyn gaar ah. Kiisaska badankood iskood ayeey iskaga baxaan. Xanuunka wadajirka ah ayaa laga yaabaa inuu ku fiicnaado NSAIDs sida naproxen. Haddii calaamaduhu kaa tagi waayaan, waxaa laguu qori karaa dawo corticosteroid ah sida prednisone.

Cudurka badanaa wuxuu iskaga roonaadaa kaligiis. Saddex meelood laba meel carruurta qaba IgA vasculitis waxay leeyihiin hal dhacdo oo keliya. Saddex meelood meel carruurta ayaa leh dhacdooyin badan. Dadku waa inay lahaadaan dabagal caafimaad oo dhow 6 bilood kadib dhacdooyinka si loo eego calaamadaha cudurka kelyaha. Dadka waaweyni waxay leeyihiin halista ugu badan ee inuu ku dhaco cudurka kalyaha ee joogtada ah.

Dhibaatooyinka waxaa ka mid noqon kara:

• Dhiigbax ku dhaca jirka gudihiisa
• Xiidmaha mindhicirka (carruurta)
  
• Dhibaatooyinka kilyaha (xaaladaha dhifka ah)

Wac adeeg bixiyahaaga haddii:

• Waxaad isku aragtaa calaamadaha IgA vasculitis, waxayna sii socdaan in ka badan dhowr maalmood.
• Waxaad leedahay kaadi midab leh ama soo bax kaadi yar.

Immunoglobulin A vaskulitis; Leukocytoclastic vaskulitis; Henoch-Schönlein purpura; HSP

• Henoch-Schonlein purpura lugaha hoose
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura
• Henoch-Schonlein purpura oo ku taal cagta ilmaha yar
• Henoch-Schonlein purpura lugaha dhallaanka
• Henoch-Schonlein purpura lugaha dhallaanka
• Henoch-Schonlein purpura lugaha

Arntfield RT, Hicks CM. Nidaamka lupus erythematosus iyo vasculitides. Gudaha: Walls RM, Hockberger RS, Gausche-Hill M, eds. Daawada Degdega ah ee Rosen: Fikradaha iyo Tababarka Caafimaadka. 9aad. Philadelphia, PA: Elsevier; 2018: cutubka 108.

Dinulos JGH. Ciladaha xasaasiyadda iyo vaskulitis. Gudaha: Habif TP, Dinulos JGH, Chapman MS, Zug KA, eds. Cudurka Maqaarka: Ciladda iyo Daaweynta. 4aad. Philadelphia, PA: Elsevier; 2018: cutubka 11.

Feehally J, FLoege J. Immunoglobulin A nephropathy iyo IgA vasculitis (Henoch-Schönlein purpura). Gudaha: Feehally J, Floege J, Tonelli M, Johnson RJ, eds. Neefroloji Caafimaad oo dhameystiran. 6aad ed. Philadelphia, PA: Elsevier; 2019: cutubka 23.

Hahn D, Hodson EM, Willis NS, Craig JC. Waxqabadyada ka hortagga iyo daaweynta cudurka kalyaha ee Henoch-Schönlein purpura (HSP). Macluumaadka Cochrane Syst Rev. 2015; (8): CD005128. PMID: 26258874 www.ncbi.nlm.nih.gov/pubmed/ 26258874.

Lu S, Liu D, Xiao J, et al. Isbarbardhigga u dhexeeya dadka waaweyn iyo carruurta Henoch-Schönlein purpura nephritis. Pediatr Nephrol. 2015; 30 (5): 791-796. PMID: 25481021 www.ncbi.nlm.nih.gov/pubmed/25481021.

Patterson JW. Qaabka falcelinta vasculopathic. Gudaha: Patterson JW, ed. Cudurka Maqaarka ee Weedon. 4aad. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: cutubka 8.

Sunderkötter CH, Zelger B, Chen KR, iyo al. Magacaabista Vasculitis-ka maqaarka: Ku darista cudurka 'Dermatologic' ee shirkii dib-u-heshiisiinta Caalamiga ah ee 'Chapel Hill Consensus Conference Nomenclature' ee Vasculitides. Arthritis Rheumatol. 2018; 70 (2): 171-184. PMID: 29136340 www.ncbi.nlm.nih.gov/pubmed/29136340.