Biliary atresia

Biliary atresia waa xannibaad ku jira tuubooyinka (marinnada) qaada dareeraha loo yaqaan 'bile' ee beerka illaa xameetida.

Cudurka 'Biliary atresia' wuxuu dhacaa marka dheecaanka xiidmaha gudaha ama banaanka beerka ay si aan caadi ahayn u cidhiidhyaan, xanniban yihiin, ama maqan yihiin. Mindhicirada xiidmaha waxay qaadaan dheecaanka dheef-shiidka ee ka yimaada beerka illaa mindhicirka yar si ay u kala jabaan dufanka isla markaana ay uga sifeeyaan qashinka jirka.

Sababta cudurka ma cadda. Waxaa laga yaabaa inay sabab u tahay:

• Infekshinka fayraska dhalashada kadib
• Soo-gaadhista walxaha sunta ah
• Waxyaabo badan oo hidde ah
• Dhaawaca umusha
• Daawooyinka qaarkood sida carbamazepine

Wuxuu si caadi ah u saameeyaa dadka ka soo jeeda Bariga Aasiya iyo Afrikaanka-Mareykanka.

Mindhicirada xiidmaha waxay caawiyaan ka saarida qashinka beerka waxayna qaadaan cusbada ka caawisa xiidmaha yar inay jabsadaan (dheef shiidaan) baruurta.

Cunnuga qaba atresia biliary, socodka bile ee ka yimaada beerka ilaa xameetida ayaa la xiraa. Tani waxay u horseedi kartaa dhaawaca beerka iyo cirrhosis-ka beerka, oo noqon kara mid dilaa ah.

Astaamuhu badanaa waxay bilaabaan inay dhacaan inta udhaxeysa 2 ilaa 8 todobaad. Cagaarshow (midab huruud ah u leh maqaarka iyo xuubka xabka) ayaa si tartiib ah u kobcaya 2 illaa 3 toddobaad dhalashada ka dib. Cunuga ayaa laga yaabaa inuu culeyskiisu kordho bisha ugu horeysa. Intaas kadib, cunuga wuu lumin doonaa wuuna xanaaqi doonaa, wuxuuna yeelan doonaa cagaarshow.

Calaamadaha kale waxaa ka mid noqon kara:

• Kaadi madow
• Calool Barar
• Saxaro udgoon iyo sabayn
• Saxaro midabkeedu yahay cirro ama dhoobo
• Si tartiib tartiib ah

Bixiyaha xanaanada caafimaadkaaga ayaa qaadi doona taariikhda caafimaad ee canugaaga wuxuuna sameyn doonaa baaritaan jireed si loo hubiyo beerka u weynaaday.

Tijaabooyinka lagu ogaanayo infekshanka jilitaanka waxaa ka mid ah:

• Raajo caloosha ah si loo hubiyo beerka iyo beeryarada weynaaday
• Ultrasound caloosha si loo hubiyo xubnaha gudaha
• Tijaabooyinka dhiigga si loo hubiyo wadarta iyo tooska heerarka bilirubin
• Sawirka 'Hepatobiliary scintigraphy' ama 'HIDA scan' si loo hubiyo in kaadi mareenka iyo xameetida ay si sax ah u shaqeynayaan
• Cad ka-qaadista beerka si loo hubiyo darnaanta cudurka cirrhosis ama meesha looga saaro sababaha kale ee cagaarshowga
• Raajo xiidmaha xiidmaha (cholangiogram) si loo hubiyo haddii marinnada xiidmaha la furay ama la xiray

Qalliin loo yaqaan habka Kasai ayaa loo sameeyaa si loogu xiro beerka mindhicirka yar. Marinnada aan caadiga ahayn waa la hareer maray. Qalliinka waa lagu guuleystaa haddii la sameeyo ka hor inta ilmuhu gaarin 8 toddobaad.

Beerka beerista ayaa weli loo baahan karaa kahor da'da 20 da'da inta badan kiisaska.

Qalliinka hore wuxuu hagaajin doonaa badbaadada in ka badan saddex meelood meel carruurta dhasha xaaladan. Faa'iidada muddada-dheer ee beerka ku-tallaalidda beerka weli lama oga, laakiin waxaa la filayaa inay wanaajiso badbaadada.

Dhibaatooyinka waxaa ka mid noqon kara:

• Caabuq
• Cirrhosis aan laga soo kabsan karin
• Beerka oo xumaada
• Dhibaatooyinka qalliinka, oo ay ku jiraan fashilka nidaamka Kasai

Wac daryeel bixiyahaaga haddii cunuggaagu u muuqdo cagaarshow, ama haddii astaamo kale oo xiiqda 'biliary atresia' ay soo baxaan.

Dhallaanka cagaarshowga - biliary atresia; Cudurka cagaarshowga cusub - biliary atresia; Ductopenia dheeriga ah; Cholangiopathy oo tirtiraysa horumarka

• Cagaarshow cusub - dheecaan
• Cagaarshowga cusub - waxa aad weydiiso dhakhtarkaaga

• Bile laga soo saaray beerka

Berlin SC. Sawir-baadhis lagu ogaanayo qofka dhasha ah. Gudaha: Martin RJ, Fanaroff AA, Walsh MC, eds. Fanaroff iyo Martin ee Neonatal-Perinatal Medicine. 11aad. Philadelphia, PA: Elsevier; 2020: baab 38.

Cazares J, Ure B, Yamataka A. Biliary atresia. Gudaha: Holcomb GW, Murphy JP, St. Peter SD, eds. Holcomb iyo Qalliinka Carruurta ee Ashcraft. 7aad ed. Philadelphia, PA: Elsevier; 2020: cutubka 43.

Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC. Cholestasis. Gudaha: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Buugga Buugga Caafimaadka Caruurta. 21aad ed. Philadelphia, PA: Elsevier; 2020: baab 383.

O’Hara SM. Beerka carruurta iyo beeryarada. Gudaha: Rumack CM, Levine D, eds. Ultrasound Baarista. 5aad. Philadelphia, PA: Elsevier; 2018: cutubka 51.