Qoraa: Janice Evans
Taariikhda Abuurista: 26 Julay 2021
Taariikhda Cusboonaysiinta: 12 Julay 2025
Anonim
Fibrous Dysplasia - Everything You Need To Know - Dr. Nabil Ebraheim
Dareemoleyad: Fibrous Dysplasia - Everything You Need To Know - Dr. Nabil Ebraheim

Fibrous dysplasia waa cudur ku dhaca lafaha kaas oo baabiiya kuna badala lafta caadiga ah unugyada laf dhabarta. Hal ama in ka badan oo lafo ah ayaa saameyn kara.

Fibrous dysplasia badanaa waxay dhacdaa caruurnimada. Dadka badankood waxay leeyihiin calaamado markay gaadhaan 30 jir. Cudurku wuxuu badanaa ku dhacaa dumarka.

Fibrous dysplasia waxay kuxirantahay dhibaatada hiddo sidaha (gen mutation) ee xakameynaya unugyada soosaara lafaha. Isbeddelku wuxuu dhacaa marka ilmuhu ku soo baxo ilmo galeenka. Xaaladaas waalid ugama gudbin ilmaha.

Calaamadaha waxaa ka mid noqon kara mid ka mid ah kuwan soo socda:

  • Lafa xanuun
  • Nabaro lafo ah
  • Dhibaatooyinka qanjidhada 'Endocrine' (hoormoonka)
  • Jabka ama cilladaha lafaha
  • Midab maqaarka oo aan caadi aheyn (midabeyn), oo ku dhaca McCune-Albright syndrome

Dhaawacyada lafaha ayaa laga yaabaa inay joogsadaan markii ilmuhu qaan gaaro.

Bixiyaha xanaanada caafimaadka ayaa sameyn doona baaritaan jireed. Raajooyin lafaha ah ayaa lagaa qaadayaa. MRI ayaa lagula talin karaa.

Ma jirto wax daawo ah oo loo yaqaan 'fibre dysplasia'. Jabka ama cilladaha lafaha ayaa loola dhaqmaa sidii loogu baahdo. Dhibaatooyinka hoormoonka ayaa u baahan in la daweeyo.


Aragtida waxay kuxirantahay darnaanta xaalada iyo astaamaha dhacaya.

Waxay kuxirantahay lafaha ay saameeyeen, dhibaatooyinka caafimaad ee ka dhalan kara waxaa ka mid ah:

  • Haddii lafta qalfoofku waxyeello gaadho, waxaa jiri kara aragti ama maqal la'aan
  • Haddii laf lugta ay saameyn ku yeelato, waxaa jiri kara dhibaato socodka iyo dhibaatooyinka wadajirka ah sida arthritis

Wac daryeel bixiyahaaga haddii cunugaaga uu leeyahay astaamo xaaladan ah, sida jabka lafaha oo soo noqnoqda iyo cilladaha lafaha oo aan la ogeyn.

Khabiiro ku takhasusay orthopedics, endocrinology, iyo genetics ayaa laga yaabaa inay ku lug yeeshaan ogaanshaha iyo daryeelka ilmahaaga.

Ma jiro waddo la yaqaan oo looga hortagi karo dysplasia fibrous. Daaweyntu waxay ujeedadeedu tahay in laga hortago dhibaatooyinka, sida jabka soo noqnoqda ee lafaha, si looga caawiyo in xaaladdu ka sii darto.

Hyperplasia oo ah barar caabuq leh; Idiopathic fibrous hyperplasia; Cudurka McCune-Albright

  • Anatomy qalfoofka hore

Czerniak B. Fibrous dysplasia iyo dhaawacyo la xiriira. Gudaha: Czerniak B, ed. Dorfman iyo Czerniak’s Buro Burooyinka. 2aad ed. Philadelphia, PA: Elsevier Saunders; 2016: cutubka 8.


Heck RK, Qalabka Ciyaaraha. Burooyinka lafdhabarka leh iyo xaaladaha nonneoplastic ee jilitaanka burooyinka lafaha. Gudaha: Azar FM, Beaty JH, Canale ST, eds. Xarunta Campbell ee lafaha. 13aad. Philadelphia, PA: Elsevier; 2017: cutubka 25.

Ganacsade SN, Nadol JB. Muujinta Otologic ee cudurka nidaamka. Gudaha: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Qalliinka Madaxa iyo Qoorta. 6aad ed. Philadelphia, PA: Elsevier Saunders; 2015: baab 149.

Shiflett JM, Perez AJ, Waalidka AD. Dhaawacyada madaxa ee carruurta: dermoids, langerhans cell histiocytosis, fibre dysplasia, iyo lipomas. Gudaha: Winn HR, ed. Youmans iyo Qalliinka neerfaha ee Winn. 7aad ed. Philadelphia, PA: Elsevier; 2017: cutubka 219.

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