Mucopolysaccharides

Mucopolysaccharides waa silsilado dhaadheer oo molecules sonkor ah oo laga helo jirka oo dhan, badiyaa xabka iyo dareeraha agagaarka kala-goysyada. Waxaa badanaa loo yaqaan glycosaminoglycans.

Marka jirku uusan burburin karin mucopolysaccharides, xaalad loo yaqaan 'mucopolysaccharidoses' (MPS) ayaa dhacda. MPS waxaa loola jeedaa koox ka mid ah cudurada laga dhaxlo dheef-shiid kiimikaadka. Dadka qaba MPS ma hayaan wax, ama ku filan walax (enzyme) oo loo baahan yahay si loo jajabiyo silsiladaha molikuyuullada.

Foomamka MPS waxaa ka mid ah:

• MPS I (Hurler syndrome; Hurler-Scheie syndrome; Scheie syndrome)
• MPS II (Hunter syndrome)
• MPS III (Sanfilippo syndrome)
• MPS IV (Morquio syndrome)

Glycosaminoglycans; GAG

Kumar V, Abbas AK, Aster JC. Cilladaha hidaha. In: Kumar V, Abbas AK, Aster JC, eds. Robbins iyo Cotran Pathologic Aasaaska Cudurka. 9aad. Philadelphia, PA: Elsevier Saunders; 2015: cutubka 5.

Pyeritz RE. Cudurrada laga dhaxlo unugyada isku xira. Gudaha: Goldman L, Schafer AI, eds. Daawada Goldman-Cecil. 26aad. Philadelphia, PA: Elsevier; 2020: cutubka 244.

Xaraashka JW. Mucopolysaccharidoses. Gudaha: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Buugga Buugga Caafimaadka Caruurta. 21aad ed. Philadelphia, PA: Elsevier; 2020: cutubka 107.